Enteropathy. X–Linked Syndrome
Keywords:
врожденная диарея с гипериммуноглобулинемией E и отсутствием островков Лангерганса
X-сцепленное заболевание
диарея и полиэндокринопатия
congenital diarrhea with hyperimmunoglobulinemia E and absence of Langerhans Islands
X‑linked disease
diarrhea and polyendocrinopathy
Abstract
The review defines congenital diarrhea with hyperimmunoglobulinemia E and absence of Langerhans Islands, (X‑linked syndrome) describes its prevalence, etiology, pathogenesis, clinical picture, diagnosis and differential diagnosis, treatment and prognosis. The prognosis of this triad is unfavorable.



