Infant feeding in hereditary metabolic diseases
Keywords:
диетотерапия
наследственные болезни обмена веществ
фенилкетонурия
лейциноз
органические ацидурии
гомоцистинурия
галактоземия
фруктоземия
diet therapy
hereditary metabolic diseases
phenylketonuria
leucinosis
organic aciduria
homocystinuria
galactosemia
fructosemia
Abstract
The lecture presents the basic principles of diet therapy of hereditary metabolic diseases. Effective diet therapy is developed for phenylketonuria (fku), leucinosis (urine smell maple syrup), organic aciduria (methylmalonic, propionic, isovalerian and glutaric), some forms of homocystinuria, galactosemia, fructosemia, etc.Recommendations for the diet, are excluded products.The effectiveness of a combination of diet and drug therapy is shown.
How to Cite
Infant feeding in hereditary metabolic diseases. (2020). Medicine: Theory and Practice, 4(1), 52-61. https://medtheor.ru/article/view/447
